Browsing by Author "O.P. SHARMA"

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Cleido‐cranial Dysostosis — Skeletal Abnormalities
(1992) S.K. GUPTA; O.P. SHARMA; S. MALHOTRA; SANJAY GUPTA. M.B.B.S.
[No abstract available]
Cranio‐metaphyseal dysplasia
(1993) DEEPIKA GUPTA; O.P. SHARMA; A.K. CHAUDHARY; S.K. GUPTA
Cranio‐metaphyseal dysplasia in two brothers, aged fourteen and twelve, is reported. Both brothers presented with deafness, repeated episodes of cold and cough and mouth breathing. Striking craniofacial configuration consisted of hypertelorism, prominent glabella and zygomatic arches, mandibular prognathism and overgrowth of middle third of face. Both patients had genu valgum deformity. Low intelligence and poor scholastic performance present in both brothers were attributed to deafness. Radiographic features consisted of obtuse mandibular angle, defective dentition, sclerotic frontal sinuses, sclerotic mastoids and temporal bones. Splaying of metaphyses of long bones was associated with mild sclerosis. Mild degree of widening of ribs was also present. One brother also had hallux valgus deformity. The radiographic and clinical differentiation of cranio‐metaphyseal dysplasia and metaphyseal dysplasia (Pyle's disease) is highlighted. Copyright © 1993, Wiley Blackwell. All rights reserved
Craniofacial Neurofibromatosis: A Roentgen Profile
(1984) S.K. GUPTA; SARABJIT KAUR; O.P. SHARMA
Multiple radiographic projections were employed to study osseous abnormalities of the skull in twenty cases of craniofacial neurofibromatosis. Calvarial defects in the lambdoid suture were observed in eight cases. Large midline defects produced a cranium bifidum appearance in one case. Mandibular changes consisted of hypoplasia with flattening of the external contour, thinning of the body and the ramus and widening of the medial and lateral coronoid spaces. Mandibular overgrowth with a convex outer contour and increase in the vertical height was seen in one case and a large cystic lesion around three unerrupted molar teeth was seen in another case. Abnormalities were also observed in the zygomatic arch and the mastoid process. The tympanic bone was absent in three cases. A 20 degree occipitomental projection best demonstrated these abnormalities. Orbital changes consisted of enlargement, outwardly curved innominate line, indistinct lower part of the innominate line, elevated lesser wing of the sphenoid, irregular enlargement or obliteration of the superior orbital fissure and intraorbital calcification. The pituitary fossa was enlarged in two cases without evidence of raised intracranial tension. Macrocranium was observed in one case. Functional disabilities observed in some cases were conductive deafness, loss of vision, cranial nerve palsies and mental retardation. Carotid angiograms done in three cases showed tortuous branches of the external carotid artery feeding the plexiform scalp lesions. A fourth ventricle tumour was seen on ventriculography in one case which presented with hemiplegia and cerebellar signs and symptoms. Skeletal abnormalities corresponded closely to the locations of soft tissue masses indicating developmental interdependance of neuroectodermal and mesodermal derivatives. Copyright © 1984, Wiley Blackwell. All rights reserved
Marginal Artery of Drummond in Aorto‐arteritis
(1984) S.K. GUPTA; A.K. AGRAWAL; O.P. SHARMA; ARVIND SRIVASTAVA
Eight cases of aorto‐arteritis with narrowing of the abdominal aorta showed a marginal artery of Drummond on aortography. There was no case with clinical evidence of abdominal angina. In six cases there was occlusion or narrowing of the superior mesenteric artery with flow of blood in the marginal artery from the inferior to the superior mesenteric artery and these patients also had hypertension resulting from involvement of renal artery/arteries. The other two patients with involvement of the inferior mesenteric artery, showed the marginal artery being filled from the superior mesenteric artery and were normotensive since there was no renal artery involvement. There were only four patients in whom the aortic arch or its branches were also involved. Two patients had evidence of active pulmonary tuberculosis. Copyright © 1984, Wiley Blackwell. All rights reserved